Disease Name:
Bronchiectasis
Alternative Names:
No information available
MeSH Description:
Persistent abnormal dilatation of the bronchi.
Type:
Clinical condition associated with amyloidosis
ICD-10 Classification
Diseases of the Respiratory System
Tissue:
Larynx, Lung, Kidney, Gastrointestinal Tract
Associated Amyloidosis:
Immunoglobulin Light-chain Amyloidosis
AA Amyloidosis
Precursor Proteins:
P0DJI8: Serum amyloid A-1 protein
Primary Name:
Serum amyloid A-1 protein
Gene Name:
SAA1
Alternative Protein Names:
Serum amyloid A-1 protein (SAA) [Cleaved into: Amyloid protein A (Amyloid fibril protein AA); Serum amyloid protein A(2-104); Serum amyloid protein A(3-104); Serum amyloid protein A(2-103); Serum amyloid protein A(2-102); Serum amyloid protein A(4-101)]
ISA Nomenclature:
AA
Protein Length:
122
Precursor Protein Sequence:
MKLLTGLVFCSLVLGVSSRSFFSFLGEAFDGARDMWRAYSDMREANYIGSDKYFHARGNYDAAKRGPGGVWAAEAISDARENIQRFFGHGAEDSLADQAANEWGRSGKDPNHFRPAGLPEKY
UniProt AC:
P0DJI8
UniProt ID:
SAA1_HUMAN
AmyPro:
AP00005
P0DJI9: Serum amyloid A-2 protein
Primary Name:
Serum amyloid A-2 protein
Gene Name:
SAA2
Alternative Protein Names:
Serum amyloid A-2 protein (SAA2)
ISA Nomenclature:
AA
Protein Length:
122
Precursor Protein Sequence:
MKLLTGLVFCSLVLSVSSRSFFSFLGEAFDGARDMWRAYSDMREANYIGSDKYFHARGNYDAAKRGPGGAWAAEVISNARENIQRLTGRGAEDSLADQAANKWGRSGRDPNHFRPAGLPEKY
UniProt AC:
P0DJI9
UniProt ID:
SAA2_HUMAN
AmyPro:
P0DOX7: Immunoglobulin kappa light chain
Primary Name:
Immunoglobulin kappa light chain
Gene Name:
IGK
Alternative Protein Names:
Immunoglobulin kappa light chain (Immunoglobulin kappa light chain EU)
ISA Nomenclature:
AL
Protein Length:
214
Precursor Protein Sequence:
DIQMTQSPSTLSASVGDRVTITCRASQSINTWLAWYQQKPGKAPKLLMYKASSLESGVPSRFIGSGSGTEFTLTISSLQPDDFATYYCQQYNSDSKMFGQGTKVEVKGTVAAPSVFIFPPSDEQLKSGTASVVCLLNNFYPREAKVQWKVDNALQSGNSQESVTEQDSKDSTYSLSSTLTLSKADYEKHKVYACEVTHQGLSSPVTKSFNRGEC
UniProt AC:
P0DOX7
UniProt ID:
IGK_HUMAN
AmyPro:
P0DOX8: Immunoglobulin lambda-1 light chain
Primary Name:
Immunoglobulin lambda-1 light chain
Gene Name:
IGL1
Alternative Protein Names:
Immunoglobulin lambda-1 light chain (Immunoglobulin lambda-1 light chain MCG)
ISA Nomenclature:
AL
Protein Length:
216
Precursor Protein Sequence:
QSALTQPPSASGSLGQSVTISCTGTSSDVGGYNYVSWYQQHAGKAPKVIIYEVNKRPSGVPDRFSGSKSGNTASLTVSGLQAEDEADYYCSSYEGSDNFVFGTGTKVTVLGQPKANPTVTLFPPSSEELQANKATLVCLISDFYPGAVTVAWKADGSPVKAGVETTKPSKQSNNKYAASSYLSLTPEQWKSHRSYSCQVTHEGSTVEKTVAPTECS
UniProt AC:
P0DOX8
UniProt ID:
IGL1_HUMAN
AmyPro:
Co-deposited Proteins:
No information available