The Amyloidoses Collection

Basic Information
Disease Name: Immunoglobulin Light-chain Amyloidosis
ISA Name: AL Amyloidosis
Alternative Names:
  • Amyloidosis, Immunoglobulin Light-chain
  • Amyloidosis, Primary
  • Primary Amyloidosis
  • Primary Systemic Amyloidosis
  • Light-chain amyloidosis
  • Light Chain Associated Amyloidosis
  • Immunoglobulin light chain (AL) amyloidosis
  • Light chain (AL) amyloidosis
MeSH Description: A nonproliferative disorder of the plasma cell characterized by excessive production and misfolding of immunoglobulin light chains that form insoluble amyloid fibrils (see amyloid deposits) in various tissues. Clinical features include liver failure; multiple myeloma; nephrotic syndrome; restrictive cardiomyopathy, and neuropathies.
Type: Amyloidosis
ICD-10 Classification Amyloidosis
Tissue: Kidney, Heart, Peripheral Nervous System (PNS), Autonomic Nervous System (ANS), Liver, Gastrointestinal Tract, Lung, Soft Tissues, Urinary Tract, Larynx
Precursor Proteins:
Co-deposited Proteins:
Interaction Network
Cross-References
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ICD:
OMIM:
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