ID: 45 Disease Name: Waldenstrom Macroglobulinemia Description: A lymphoproliferative disorder characterized by pleomorphic B-lymphocytes including plasma cells, with increased levels of monoclonal serum immunoglobulin M. There is lymphoplasmacytic cells infiltration into bone marrow and often other tissues, also known as lymphoplasmacytic lymphoma. Clinical features include anemia; hemorrhages; and hyperviscosity. Disease Type: Clinical conditions associated with amyloidosis ICD-10 Classification: Neoplasms Tissue: Kidney, Blood Vessel, Liver Cross References http://apps.who.int/classifications/icd10/browse/2016/en#/C88 https://meshb.nlm.nih.gov/record/ui?ui=D008258 https://www.omim.org/entry/610430 https://www.omim.org/entry/153600 https://www.ncbi.nlm.nih.gov/pubmed/2492644 https://www.ncbi.nlm.nih.gov/pubmed/6403452 https://www.ncbi.nlm.nih.gov/pubmed/8487054 https://www.ncbi.nlm.nih.gov/pubmed/6155694 https://www.ncbi.nlm.nih.gov/pubmed/11530809 https://www.ncbi.nlm.nih.gov/pubmed/9430877 https://www.ncbi.nlm.nih.gov/pubmed/23689541 Alternative Names: Familial Waldenstrom's Macroglobulinaemia Lymphoma, Lymphocytic, Plasmacytoid Lymphoma, Lymphoplasmacytoid Macroglobulinemia Primary Macroglobulinemia Waldenstrom's Macroglobulinaemia Waldenstrom's Macroglobulinemia Precursor Proteins: P0DJI8 | Serum amyloid A-1 protein P0DJI9 | Serum amyloid A-2 protein P61769 | Beta-2-microglobulin P0DOX7 | Immunoglobulin kappa light chain P0DOX8 | Immunoglobulin lambda-1 light chain Co-deposited Proteins: No information available Link to Amyloidosis: http://83.212.109.111:8084/amyco/8 http://83.212.109.111:8084/amyco/29 http://83.212.109.111:8084/amyco/33 //