ID: 64 Disease Name: Behcet Syndrome Description: Rare chronic inflammatory disease involving the small blood vessels. It is of unknown etiology and characterized by mucocutaneous ulceration in the mouth and genital region and uveitis with hypopyon. The neuro-ocular form may cause blindness and death. Synovitis; thrombophlebitis; gastrointestinal ulcerations; retinal vasculitis; and optic atrophy may occur as well. Disease Type: Clinical conditions associated with amyloidosis ICD-10 Classification: Diseases of the Musculoskeletal System and Connective Tissue Tissue: Kidney, Salivary Gland, Gastrointestinal Tract Cross References https://www.ncbi.nlm.nih.gov/pubmed/1147457 https://www.ncbi.nlm.nih.gov/pubmed/25579733 https://www.ncbi.nlm.nih.gov/pubmed/22961375 https://www.ncbi.nlm.nih.gov/pubmed/10644872 http://apps.who.int/classifications/icd10/browse/2016/en#/M35 https://meshb.nlm.nih.gov/record/ui?ui=D001528 https://www.omim.org/entry/109650 Alternative Names: Adamantiades-Behcet Disease Complex Behcet Disease Behcet Triple Symptom Complex Behcet's Syndrome Old Silk Route Disease Triple Symptom Complex Triple-Symptom Complex BD Precursor Proteins: P0DJI8 | Serum amyloid A-1 protein P0DJI9 | Serum amyloid A-2 protein Co-deposited Proteins: No information available Link to Amyloidosis: http://83.212.109.111:8084/amyco/29 //