ID: 66 Disease Name: Polyarteritis Nodosa Description: A form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized arteries, often with microaneurysms. It is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. Polyarteritis nodosa with lung involvement is called Churg-Strauss Syndrome. Disease Type: Clinical conditions associated with amyloidosis ICD-10 Classification: Diseases of the Musculoskeletal System and Connective Tissue Tissue: Kidney, Intestine Cross References https://www.ncbi.nlm.nih.gov/pubmed/26233953 https://www.ncbi.nlm.nih.gov/pubmed/24106820 https://www.ncbi.nlm.nih.gov/pubmed/10224498 https://www.ncbi.nlm.nih.gov/pubmed/27791393 http://apps.who.int/classifications/icd10/browse/2016/en#/M30 https://meshb.nlm.nih.gov/record/ui?ui=D010488 https://www.omim.org/entry/615688 Alternative Names: Polyarteritis Nodosa, Childhood-Onset PAN ADA2 Deficiency Essential Polyarteritis Necrotizing Arteritis Periarteritis Nodosa Adenosine Deaminase 2 Deficiency DADA2 Vasculitis due to DADA2 Vasculitis due to ADA2 deficiency Deficiency of Adenosine Deaminase 2 Precursor Proteins: P0DJI8 | Serum amyloid A-1 protein P0DJI9 | Serum amyloid A-2 protein Co-deposited Proteins: No information available Link to Amyloidosis: http://83.212.109.111:8084/amyco/29 //