ID: 67 Disease Name: PrP Systemic Amyloidosis Description: Disease Type: Amyloidosis ICD-10 Classification: Diseases of the Nervous System Tissue: Peripheral Nervous System (PNS), Kidney, Liver, Lung Cross References https://www.ncbi.nlm.nih.gov/pubmed/24224623 https://www.ncbi.nlm.nih.gov/pubmed/24296653 https://www.ncbi.nlm.nih.gov/pubmed/25623792 http://apps.who.int/classifications/icd10/browse/2016/en#/G60 Alternative Names: Prion protein systemic amyloidosis Chronic diarrhea with HSAN Chronic diarrhea with hereditary sensory and autonomic neuropathy Prion Disease Associated with Diarrhea and Autonomic Neuropathy Precursor Proteins: P04156 | Major prion protein Co-deposited Proteins: P02743 | Serum amyloid P-component Link to Amyloidosis: No information available //